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Hereditary Hemorrhagic Telangiectasia: Presenting with Epistaxis

Sandeep Kumar Kar, Manasij Mitra, Tanmoy Ganguly, Manabendra Sarkar, Chaitali Sen Dasgupta, Anupam Goswami

Osler-Weber-Rendu disease (OWRD) or Hereditary Hemorrhagic Telangiectasia (HHT) is a rare autosomal dominant disorder that causes muco-cutanesous and visceral vascular dysplasia and results in increased tendency for bleeding [1-4]. Patients with HHT may present with variety of symptoms and management differs accordingly. Epistaxis is the most common symptom of HHT and mucocutaneous telangiectasia the most common sign [5]. Here we describe the anesthesia management of a patient presenting with epistaxis in emergency suffering from this syndrome.